Caffey's Disease Case Study

ABSTRACT: Caffey’s disease or Infantile Cortical Hyperostosis is a rare, mostly self-limiting disease, affecting young infants less than 6 months of age. It is characterized by a triad of soft tissue swelling, cortical thickening of the underlying bone and hyperirritability. The mean age of presentation is 9-11 weeks of age. It typically involves the mandible, clavicles, ribs and diaphysis of the long bones. We report a case of Caffey's disease presenting at an early age of 6 weeks, affecting long bones, with symmetrical involvement of ulnar bones, and thrombocytosis an uncommon presentation. On follow up for 48 months there were no recurrences.
Caffey's disease, also called as infantile cortical hyperostosis (ICH), is characterized by an episode of massive sub periosteal new bone

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