Abstract
Rhabdomyosarcomas are malignant skeletal muscle tumors. They account for about 50% of soft tissue sarcomas in children. The usual sites include head and neck(35%),extremities, trunk,retroperitoneum. Lesser common sites include the genitourinary. The cervix is one of the least common sites in genitourinary tract.We report a case of Cervical Rhabdomyosarcoma who was misdiagnosed as Vaginal RMS and was started on chemotherapy. We had to do an emergency excision of the mass,when she developed excessive bleeding per vaginum.
Keywords
Embryonal Rhabdomyosarcomas,Cervical Rhabdomyosarcomas,
Background
Rhabdomyosarcomas are malignant skeletal muscle tumors and account for about 50% of soft tissue sarcomas in children. The Intergroup Rhabdomyosarcoma Study Group divided it into three major histologic subtypes: Embryonal(ERMS), alveolar, and undifferentiated. The most common sites include head and neck(35%),extremities, trunk, retroperitoneum. Lesser common sites are the genitourinary. The cervix is one of the least common sites in genitourinary tract. Vagina is involved more commonly than cervix. The most common type is embryonal subtype, and accounts for 68% of all cases.Patient presents with mass filling the vagina and sometimes protruding out of introitus.
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Undifferentiated type is the rarest with worst prognosis.
A multimodality treatment approach including surgery, chemotherapy and radiotherapy has evolved over time with a 60% overall survival.The survival for localised disease is